Congenital Midline Cervical Cleft: A Variant of Tessier Number 30 Cleft Causing Micrognathia.

Cleft Palate Craniofac J

Hospital for Rehabilitation of Craniofacial Anomalies and Hospital of Clinics of Medicine Faculty, University of São Paulo, Brazil.

Published: November 2021


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Article Abstract

Congenital midline cervical cleft is a rare and generally isolated malformation of the ventral neck region with no clear etiology established. Mandibular deformities, such as micrognathia, could be considered as a consequence of a cleft cervical contracture. Complete surgical excision of the subcutaneous fibrous cord at an early age is the primary treatment modality, minimizing growth development problems on surrounding affected tissue. The aim of this study is to describe the clinical, surgical, and histological findings in a female child with congenital midline cervical cleft along with a relevant literature review. Three years follow-up after surgery exhibited satisfactory functional and cosmetic results.

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http://dx.doi.org/10.1177/1055665620987412DOI Listing

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