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Article Abstract
Background: Although we and others have reported cases of patients with Anderson-Fabry disease (AFD) complicated by coronary spastic angina (CSA), the prevalence of CSA in these patients remains unknown.
Methods and results: We performed the acetylcholine-induced provocation test, according to the Japanese guidelines for the diagnosis and treatment of patients with CSA, in 9 consecutive patients having 5 independent AFD pedigrees. Coronary spasms were provoked in conjunction with symptoms and ECG ischemic changes in 8 of 9 (89%) patients with AFD.
Conclusions: We found an unexpectedly high prevalence of CSA in patients with AFD.
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| http://dx.doi.org/10.1253/circj.CJ-18-0734 | DOI Listing |
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