Entangled: Rapunzel syndrome with postoperative intussusception.

J Surg Case Rep

Nursing and Midwifery Research Department (NMRD), Hamad Medical Corporation, PO Box 3050, Doha, Baladiyat ad Dawhah, Qatar.

Published: October 2024


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Article Abstract

We present a case of a 7-year-old girl with Rapunzel syndrome, a rare complication of trichobezoar, initially presenting with nonspecific symptoms. Diagnostic challenges led to delayed intervention. Surgical removal of the trichobezoar was successful, but postoperative complications included jejunojejunal intussusception, highlighting the necessity for vigilant follow-up and comprehensive psychiatric evaluation. The emergence of intussusception emphasizes the profound impact of underlying psychiatric disorders, such as trichotillomania and trichophagia, which contribute to trichobezoar formation. These conditions necessitate ongoing psychiatric management to address behavioral factors that predispose to recurrent bezoar formation and associated gastrointestinal complications. Effective follow-up strategies should encompass immediate postoperative care and long-term psychiatric support to optimize patient outcomes and minimize the risk of recurrent intussusception.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11449833PMC
http://dx.doi.org/10.1093/jscr/rjae623DOI Listing

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