Cochlear Implant in Klippel-Feil Syndrome: Challenges and Concerns.

Indian J Otolaryngol Head Neck Surg

Department of Otolaryngology, Otology, Neurotology and Cochlear Implant Unit, Christian Medical College, Vellore, Tamil Nadu 632004 India.

Published: December 2022


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Article Abstract

Cochlear implantation (CI) can be safely performed in patients with syndromic hearing loss. Here we present a case of CI in a child with Klippel-Feil syndrome with various skeletal, extraskeletal, cochleovestibular and Arnold-Chiari malformations. Multidisciplinary approach and good preoperative imaging play a key role in planning for surgery.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9895708PMC
http://dx.doi.org/10.1007/s12070-021-02728-0DOI Listing

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