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Cor Triatriatum Dexter (CTD) is a rare congenital anomaly involving the systemic venous valves. Failure of regression of the right-sided sinus venosus valve leads to abnormal septation of the right atrium and a variety of right atrial and tricuspid valve obstructive lesions. The presentation can be varied ranging from asymptomatic to persistent neonatal cyanosis. We describe a late diagnosis of CTD in a 10-month-old male with persistent hypoxia despite balloon valvuloplasty for mild pulmonic valve stenosis with a large secundum atrial septal defect and a mildly hypoplastic right ventricle.
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http://dx.doi.org/10.1111/echo.14175 | DOI Listing |
Cureus
August 2025
Physiology, Alkindy College of Medicine, Baghdad University, Baghdad, IRQ.
Cor triatriatum is a rare congenital heart defect that divides the right or left atrium into three chambers. Although the diagnosis is typically made within the first years of birth, it can occasionally be made later in adulthood and is frequently associated with other cardiac defects but may be present in isolation. Clinical manifestations range from lung congestion, exhaustion, coughing, and dyspnea to the onset of heart failure.
View Article and Find Full Text PDFIndian J Pediatr
August 2025
Department of Radiodiagnosis and Imaging, Postgraduate Institute of Medical Education and Research, Sector-12, Chandigarh, 160012, India.
Ann Pediatr Cardiol
July 2025
Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.
Atrioventricular septal defect (AVSD) with cor triatriatum sinister (CTS) is a rare congenital anomalous combination. Few cases of AVSD and CTS have been reported in the literature. However, an isolated case of CTS with partial AVSD, left superior vena cava, and unroofed coronary sinus in an adult has not been reported in the literature.
View Article and Find Full Text PDFBraz J Cardiovasc Surg
August 2025
Department of Cardiovascular Medicine, Hunan Provincial People's Hospital (Hunan Normal University First Affiliated Hospital), Changsha, Hunan, People's Republic of China.
This case study involves a 51-year-old woman with a complex cardiovascular condition, namely cor triatriatum dexter, accompanied by sick sinus syndrome. She presented with bradycardia, dizziness, and amaurosis, and was admitted to the emergency department due to right limb numbness. Diagnostic examinations, including computed tomography and cardiac color ultrasound screening, revealed the presence of cor triatriatum dexter with an enlarged left atrium and ventricle.
View Article and Find Full Text PDFCureus
July 2025
Cardiology, Novant Health, Winston-Salem, USA.
Cor triatriatum sinister (CTS) is a rare congenital anomaly characterized by a fibromuscular membrane that divides the left atrium into proximal and distal chambers. Typically, the pulmonary veins drain into the proximal chamber, while the distal chamber remains continuous with the left atrial appendage and the mitral valve. Communication between the two chambers occurs through one or more fenestrations of variable size.
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