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Article Abstract
We report a child with osteopetrosis, oxycephaly and Chiari type I malformation who presented with raised intracranial pressure. During cranial expansion surgery the patient developed sudden cardiac arrest which we believe was probably related to the Chiari malformation. The case highlights a previously unrecognized association between osteopetrosis, craniosynostosis and a persistently open fontanelle at age 4 years. In addition it supports the existing literature in emphasizing the need for careful preoperative work up, choice of approach and operative technique in children with complex craniosynostosis and Chiari malformation.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2740010 | PMC |
| http://dx.doi.org/10.4076/1757-1626-2-6787 | DOI Listing |
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