A case of esophageal atresia with the bronchial-like lower esophagus which originates from the left lower lobe bronchus.

Background: Esophageal atresia with or without a trachea-esophageal fistula occurs due to the failure of separation or incomplete development of the foregut. Therefore, esophageal atresia is often associated with various forms of tracheobronchial anomalies. We report an extremely rare case of esophageal atresia.

The "Twitching Technique": A New Space-Irrespective Laparoscopic Ligation Technique Using a JAiMY Needle Holder.

Laparoscopic intracorporeal sutures and knots require advanced techniques in children. The JAiMY needle holder (Endocontrol Company, Grenoble, France), a flexible jaw with both clockwise and anticlockwise revolving functions, enables the placement of sutures in very small working spaces. Using this tool, a novel new ligation method, which we named "twitching technique," can be performed.

Novel PHOX2B mutations in congenital central hypoventilation syndrome.

Background: Congenital central hypoventilation syndrome (CCHS) is caused by mutation of paird-like homeobox 2B (PHOX2B). Approximately 90% of patients were found to carry polyalanine repeat expansion mutation (PARM), and the remaining 10% had non-PARM (NPARM). In PARM, the length of the polyalanine expansion correlates with clinical disease severity.

Features and Techniques of Laparoscopic Percutaneous Extraperitoneal Closure for Ovarian Hernia.

Purpose: The purpose of this report was to evaluate the safety and efficacy of the simple laparoscopic percutaneous extraperitoneal closure (LPEC) method for treating ovarian hernia patients, including newborns and low-birth-weight infants.

Methods: We retrospectively reviewed the cases of ovarian hernia that were treated in our institution from May 2012 to September 2017.

Results: Thirty-four infants were included in this study (right side, n = 8; left side, n = 22; bilateral, n = 4).

Transumbilical Surgery for Duodenal Stenosis in a Child with Situs Inversus: The First Report.

. Situs inversus is a rare congenital anomaly with a reported incidence of only 1 in 5,000 to 10,000 live births. Congenital duodenal stenosis complicated with situs inversus is an even rarer entity.

A case of recurrent and synchronous fibrous hamartoma of infancy.

We retrospectively reviewed the chart of a patient with recurrent fibrous hamartoma of infancy (FHI). This lesion presented as a gradually enlarging mass on the child's buttock. The child, a 6-month-old male, was followed up, and at 19 months of age the mass was excised.

Primary megaureter: results of surgical treatment.

Background: The aim of this study was to assess the clinical and radiological outcome after surgical treatment for primary -megaureter.

Methods: A retrospective analysis of 16 patients who had reimplantation of 17 primary megaureters between January 1997 and April 2001 was performed. Patients who had additional urinary tract pathology were not included in this study.

Congenital posterior urethral obstruction: re-do fulguration.

In patients with congenital posterior urethral obstruction, transurethral fulguration (TUF) is usually the treatment of choice if the patient is in a stable condition. However, few papers have described the proportion of patients who need further fulguration. We reviewed 83 boys with a congenital obstructive posterior urethral membrane (COPUM) to assess the role of re-do fulguration, as judged by prospective video recordings.